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KMID : 0359919930120040698
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Korean Journal of Nephrology
1993 Volume.12 No. 4 p.698 ~ p.704
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A Case of Hereditary Coproporphyria with Renal Insufficiency
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강재황
함종렬/정판준/김성욱/심대석/김정렬/김호철/이근홍/황일용
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Abstract
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We report a case of hereditary coproporphyria with real insufficiency in a 20 years old girl who had frequent abdominal pain. The typical clinical and biochemical findings of hepatic porphyria represent the hereditary coproporphyria, most likely.
Her
symptoms and signs were clearly exacerbated in a relation to the menstrual cycle. During admission, serum creatinine change up to 3.8 mg/dl. Until 35 days after discharge, she was found to have persistently elevated serum creatinine
concentration.
On
the renal biopsy, there was chronic Tubulo-Interstitis, which presented with focal mild degree interstitial edema, chronic inflammatory cells infiltriton, and vacuolization of tubular cells. Possible etiologic factors including porphyria or its
precursor itself for the ienal insufficiency of this patient (HCP) should be discussed.
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KEYWORD
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